Class information for:
Level 1: SPINOCEREBELLAR ATAXIA//MACHADO JOSEPH DISEASE//SCA2

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
2557 2208 34.3 81%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
603 3       HUNTINGTONS DISEASE//SPINOCEREBELLAR ATAXIA//POLYGLUTAMINE 14359
1711 2             SPINOCEREBELLAR ATAXIA//HEREDITARY SPASTIC PARAPLEGIA//FRIEDREICHS ATAXIA 6674
2557 1                   SPINOCEREBELLAR ATAXIA//MACHADO JOSEPH DISEASE//SCA2 2208

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 SPINOCEREBELLAR ATAXIA authKW 2580914 15% 58% 321
2 MACHADO JOSEPH DISEASE authKW 1470470 7% 69% 154
3 SCA2 authKW 870324 3% 85% 74
4 SPINOCEREBELLAR ATAXIA TYPE 2 authKW 684044 3% 85% 58
5 AUTOSOMAL DOMINANT CEREBELLAR ATAXIA authKW 650331 2% 87% 54
6 CAG REPEAT authKW 397888 5% 27% 105
7 DENTATORUBRAL PALLIDOLUYSIAN ATROPHY authKW 395052 2% 71% 40
8 SCA6 authKW 378581 2% 74% 37
9 SCA3 authKW 318378 2% 56% 41
10 SPINOCEREBELLAR ATAXIA TYPE 3 authKW 304331 2% 51% 43

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with term
in class
1 Clinical Neurology 33951 54% 0% 1184
2 Neurosciences 7381 35% 0% 763
3 Genetics & Heredity 5318 21% 0% 469
4 Neuroimaging 378 2% 0% 39
5 Pathology 335 4% 0% 92
6 Psychiatry 249 5% 0% 109
7 Ophthalmology 46 2% 0% 42
8 Biochemistry & Molecular Biology 38 9% 0% 190
9 Radiology, Nuclear Medicine & Medical Imaging 17 2% 0% 54
10 Medicine, Research & Experimental 9 2% 0% 45

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with term
in class
1 UNIGENE 108368 1% 28% 28
2 ROSE MOSS PARKINSON NEURODEGENERAT DIS 82966 0% 100% 6
3 IBMC UNIGENE 69138 0% 100% 5
4 ROSE MOSS PARKINSONS NEURODEGENERAT DIS 61591 0% 64% 7
5 NEUROL 58975 47% 0% 1028
6 ENFERMEDADES NEUROL 57613 0% 83% 5
7 CLIN NEUROANAT 52386 1% 12% 32
8 HLTH SCI GERMANS TRIAS PUJOL IGTP 49775 0% 60% 6
9 ICBAS MED GENET 41483 0% 100% 3
10 MOL PHYSIOL BRAIN NEUROL MED 41483 0% 100% 3

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 CEREBELLUM 146729 4% 11% 98
2 MOVEMENT DISORDERS 22844 5% 2% 104
3 JOURNAL OF THE NEUROLOGICAL SCIENCES 15880 5% 1% 108
4 ARCHIVES OF NEUROLOGY 13339 4% 1% 80
5 NEUROLOGY 12842 6% 1% 141
6 JOURNAL OF NEUROLOGY 11395 3% 1% 71
7 HUMAN MOLECULAR GENETICS 6271 3% 1% 67
8 ANNALS OF NEUROLOGY 5895 3% 1% 58
9 NEUROPATHOLOGY 5527 1% 2% 24
10 BRAIN 5188 2% 1% 49

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 SPINOCEREBELLAR ATAXIA 2580914 15% 58% 321 Search SPINOCEREBELLAR+ATAXIA Search SPINOCEREBELLAR+ATAXIA
2 MACHADO JOSEPH DISEASE 1470470 7% 69% 154 Search MACHADO+JOSEPH+DISEASE Search MACHADO+JOSEPH+DISEASE
3 SCA2 870324 3% 85% 74 Search SCA2 Search SCA2
4 SPINOCEREBELLAR ATAXIA TYPE 2 684044 3% 85% 58 Search SPINOCEREBELLAR+ATAXIA+TYPE+2 Search SPINOCEREBELLAR+ATAXIA+TYPE+2
5 AUTOSOMAL DOMINANT CEREBELLAR ATAXIA 650331 2% 87% 54 Search AUTOSOMAL+DOMINANT+CEREBELLAR+ATAXIA Search AUTOSOMAL+DOMINANT+CEREBELLAR+ATAXIA
6 CAG REPEAT 397888 5% 27% 105 Search CAG+REPEAT Search CAG+REPEAT
7 DENTATORUBRAL PALLIDOLUYSIAN ATROPHY 395052 2% 71% 40 Search DENTATORUBRAL+PALLIDOLUYSIAN+ATROPHY Search DENTATORUBRAL+PALLIDOLUYSIAN+ATROPHY
8 SCA6 378581 2% 74% 37 Search SCA6 Search SCA6
9 SCA3 318378 2% 56% 41 Search SCA3 Search SCA3
10 SPINOCEREBELLAR ATAXIA TYPE 3 304331 2% 51% 43 Search SPINOCEREBELLAR+ATAXIA+TYPE+3 Search SPINOCEREBELLAR+ATAXIA+TYPE+3

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 SEIDEL, K , SISWANTO, S , BRUNT, ERP , DEN DUNNEN, W , KORF, HW , RUB, U , (2012) BRAIN PATHOLOGY OF SPINOCEREBELLAR ATAXIAS.ACTA NEUROPATHOLOGICA. VOL. 124. ISSUE 1. P. 1 -21 147 81% 75
2 SCHOLS, L , PAULSON, H , AUBURGER, G , KERMER, P , JEN, JC , SEIDEL, K , KORF, HW , DELLER, T , RUB, U , (2013) CLINICAL FEATURES, NEUROGENETICS AND NEUROPATHOLOGY OF THE POLYGLUTAMINE SPINOCEREBELLAR ATAXIAS TYPE 1, 2, 3, 6 AND 7.PROGRESS IN NEUROBIOLOGY. VOL. 104. ISSUE . P. 38 -66 173 57% 48
3 WHALEY, NR , FUJIOKA, S , WSZOLEK, ZK , (2011) AUTOSOMAL DOMINANT CEREBELLAR ATAXIA TYPE I: A REVIEW OF THE PHENOTYPIC AND GENOTYPIC CHARACTERISTICS.ORPHANET JOURNAL OF RARE DISEASES. VOL. 6. ISSUE . P. - 108 89% 19
4 MARELLI, C , CAZENEUVE, C , BRICE, A , STEVANIN, G , DURR, A , (2011) AUTOSOMAL DOMINANT CEREBELLAR ATAXIAS.REVUE NEUROLOGIQUE. VOL. 167. ISSUE 5. P. 385 -400 114 78% 5
5 DURR, A , (2010) AUTOSOMAL DOMINANT CEREBELLAR ATAXIAS: POLYGLUTAMINE EXPANSIONS AND BEYOND.LANCET NEUROLOGY. VOL. 9. ISSUE 9. P. 885-894 78 79% 175
6 SUN, YM , LU, C , WU, ZY , (2016) SPINOCEREBELLAR ATAXIA: RELATIONSHIP BETWEEN PHENOTYPE AND GENOTYPE - A REVIEW.CLINICAL GENETICS. VOL. 90. ISSUE 4. P. 305 -314 90 87% 0
7 VAN GAALEN, J , GIUNTI, P , VAN DE WARRENBURG, BP , (2011) MOVEMENT DISORDERS IN SPINOCEREBELLAR ATAXIAS.MOVEMENT DISORDERS. VOL. 26. ISSUE 5. P. 792 -800 85 85% 39
8 SCHOLS, L , BAUER, P , SCHMIDT, T , SCHULTE, T , RIESS, O , (2004) AUTOSOMAL DOMINANT CEREBELLAR ATAXIAS: CLINICAL FEATURES, GENETICS, AND PATHOGENESIS.LANCET NEUROLOGY. VOL. 3. ISSUE 5. P. 291-304 91 67% 458
9 PARK, H , KIM, HJ , JEON, BS , (2015) PARKINSONISM IN SPINOCEREBELLAR ATAXIA.BIOMED RESEARCH INTERNATIONAL. VOL. . ISSUE . P. - 73 96% 2
10 MATILLA-DUENAS, A , CORRAL-JUAN, M , VOLPINI, V , SANCHEZ, I , (2012) THE SPINOCEREBELLAR ATAXIAS: CLINICAL ASPECTS AND MOLECULAR GENETICS.NEURODEGENERATIVE DISEASES. VOL. 724. ISSUE . P. 351-374 80 83% 24

Classes with closest relation at Level 1



Rank Class id link
1 26667 TANDOSPIRONE CITRATE//CORTICAL CEREBELLAR ATROPHY//NEUROBEHAV NEUROBIOL NEUROPSYCHOL UNIT
2 377 HUNTINGTONS DISEASE//HUNTINGTIN//POLYGLUTAMINE
3 16834 SECT GENE STRUCT DIS//REPEAT INSTABILITY//MUTS BETA
4 20207 KENNEDYS DISEASE//SPINAL AND BULBAR MUSCULAR ATROPHY//SBMA
5 22273 ARSACS//AOA2//SENATAXIN
6 3134 FRATAXIN//FRIEDREICHS ATAXIA//FRIEDREICH ATAXIA
7 8349 MULTIPLE SYSTEM ATROPHY//STRIATONIGRAL DEGENERATION//GLIAL CYTOPLASMIC INCLUSIONS
8 34928 PERRAULT SYNDROME//HOLMES ATAXIA//BOUCHER NEUHAUSER SYNDROME
9 9176 HEREDITARY SPASTIC PARAPLEGIA//SPASTIN//SPG4
10 34141 NEURONAL INTRANUCLEAR INCLUSION DISEASE//INTRANUCLEAR INCLUSION BODY DISEASE//NEURONAL INTRANUCLEAR HYALINE INCLUSION DISEASE

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