Class information for:
Level 1: HEREDITARY SPASTIC PARAPLEGIA//SPASTIN//SPG4

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
9176 1181 35.2 86%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
603 3       HUNTINGTONS DISEASE//SPINOCEREBELLAR ATAXIA//POLYGLUTAMINE 14359
1711 2             SPINOCEREBELLAR ATAXIA//HEREDITARY SPASTIC PARAPLEGIA//FRIEDREICHS ATAXIA 6674
9176 1                   HEREDITARY SPASTIC PARAPLEGIA//SPASTIN//SPG4 1181

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 HEREDITARY SPASTIC PARAPLEGIA authKW 4993558 21% 78% 249
2 SPASTIN authKW 1573040 6% 82% 74
3 SPG4 authKW 1372068 5% 96% 55
4 SPG11 authKW 830194 3% 94% 34
5 HEREDITARY SPASTIC PARAPARESIS authKW 776057 3% 73% 41
6 SPASTIC PARAPLEGIA authKW 636993 4% 46% 53
7 SPAST authKW 542932 2% 100% 21
8 THIN CORPUS CALLOSUM authKW 481274 2% 85% 22
9 ATLASTIN authKW 466661 2% 95% 19
10 SPATACSIN authKW 415097 1% 94% 17

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Clinical Neurology 9900 40% 0% 473
2 Genetics & Heredity 3743 24% 0% 285
3 Neurosciences 1409 22% 0% 258
4 Cell Biology 1390 19% 0% 224
5 Biochemistry & Molecular Biology 271 17% 0% 198
6 Psychiatry 78 4% 0% 48
7 Pediatrics 33 3% 0% 34
8 Pathology 25 2% 0% 24
9 Neuroimaging 21 1% 0% 8
10 Developmental Biology 12 1% 0% 12

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 CELLULAR NEUROL UNIT 176260 1% 45% 15
2 GENET CYTOGENET 93163 3% 11% 32
3 UMR S679 75610 1% 21% 14
4 NEUROGENET BRANCH 73575 2% 11% 27
5 FEDERAT NEUROSCI IFR70 59091 0% 57% 4
6 MED GENETSECT NEUROGENET 58170 0% 75% 3
7 NEUROL B NEUROGENET UNIT 51708 0% 100% 2
8 PHYS BIOPHYS E22 46535 0% 60% 3
9 NEUROSCI MED BIOTECHNOL 45958 0% 44% 4
10 U679 43515 1% 11% 16

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 NEUROGENETICS 38467 3% 5% 30
2 EUROPEAN JOURNAL OF NEUROLOGY 4483 2% 1% 26
3 JOURNAL OF NEUROLOGY 4318 3% 1% 32
4 AMERICAN JOURNAL OF HUMAN GENETICS 4122 3% 0% 36
5 JOURNAL OF THE NEUROLOGICAL SCIENCES 4048 3% 0% 40
6 NEUROLOGY 3896 5% 0% 57
7 HUMAN MOLECULAR GENETICS 2839 3% 0% 33
8 BRAIN 2323 2% 0% 24
9 JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY 2286 2% 0% 29
10 EUROPEAN JOURNAL OF HUMAN GENETICS 2266 2% 0% 18

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 HEREDITARY SPASTIC PARAPLEGIA 4993558 21% 78% 249 Search HEREDITARY+SPASTIC+PARAPLEGIA Search HEREDITARY+SPASTIC+PARAPLEGIA
2 SPASTIN 1573040 6% 82% 74 Search SPASTIN Search SPASTIN
3 SPG4 1372068 5% 96% 55 Search SPG4 Search SPG4
4 SPG11 830194 3% 94% 34 Search SPG11 Search SPG11
5 HEREDITARY SPASTIC PARAPARESIS 776057 3% 73% 41 Search HEREDITARY+SPASTIC+PARAPARESIS Search HEREDITARY+SPASTIC+PARAPARESIS
6 SPASTIC PARAPLEGIA 636993 4% 46% 53 Search SPASTIC+PARAPLEGIA Search SPASTIC+PARAPLEGIA
7 SPAST 542932 2% 100% 21 Search SPAST Search SPAST
8 THIN CORPUS CALLOSUM 481274 2% 85% 22 Search THIN+CORPUS+CALLOSUM Search THIN+CORPUS+CALLOSUM
9 ATLASTIN 466661 2% 95% 19 Search ATLASTIN Search ATLASTIN
10 SPATACSIN 415097 1% 94% 17 Search SPATACSIN Search SPATACSIN

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 LO GIUDICE, T , LOMBARDI, F , SANTORELLI, FM , KAWARAI, T , ORLACCHIO, A , (2014) HEREDITARY SPASTIC PARAPLEGIA: CLINICAL-GENETIC CHARACTERISTICS AND EVOLVING MOLECULAR MECHANISMS.EXPERIMENTAL NEUROLOGY. VOL. 261. ISSUE . P. 518 -539 151 67% 42
2 FINK, JK , (2013) HEREDITARY SPASTIC PARAPLEGIA: CLINICO-PATHOLOGIC FEATURES AND EMERGING MOLECULAR MECHANISMS.ACTA NEUROPATHOLOGICA. VOL. 126. ISSUE 3. P. 307-328 140 67% 85
3 FINSTERER, J , LOSCHER, W , QUASTHOFF, S , WANSCHITZ, J , AUER-GRUMBACH, M , STEVANIN, G , (2012) HEREDITARY SPASTIC PARAPLEGIAS WITH AUTOSOMAL DOMINANT, RECESSIVE, X-LINKED, OR MATERNAL TRAIT OF INHERITANCE.JOURNAL OF THE NEUROLOGICAL SCIENCES. VOL. 318. ISSUE 1-2. P. 1-18 118 81% 78
4 KLEBE, S , STEVANIN, G , DEPIENNE, C , (2015) CLINICAL AND GENETIC HETEROGENEITY IN HEREDITARY SPASTIC PARAPLEGIAS: FROM SPG1 TO SPG72 AND STILL COUNTING.REVUE NEUROLOGIQUE. VOL. 171. ISSUE 6-7. P. 505 -530 141 71% 8
5 TESSON, C , KOHT, J , STEVANIN, G , (2015) DELVING INTO THE COMPLEXITY OF HEREDITARY SPASTIC PARAPLEGIAS: HOW UNEXPECTED PHENOTYPES AND INHERITANCE MODES ARE REVOLUTIONIZING THEIR NOSOLOGY.HUMAN GENETICS. VOL. 134. ISSUE 6. P. 511 -538 121 61% 8
6 SALINAS, S , PROUKAKIS, C , CROSBY, A , WARNER, TT , (2008) HEREDITARY SPASTIC PARAPLEGIA: CLINICAL FEATURES AND PATHOGENETIC MECHANISMS.LANCET NEUROLOGY. VOL. 7. ISSUE 12. P. 1127-1138 92 75% 212
7 FINK, JK , (2006) HEREDITARY SPASTIC PARAPLEGIA.CURRENT NEUROLOGY AND NEUROSCIENCE REPORTS. VOL. 6. ISSUE 1. P. 65 -76 88 82% 144
8 SOLOWSKA, JM , BAAS, PW , (2015) HEREDITARY SPASTIC PARAPLEGIA SPG4: WHAT IS KNOWN AND NOT KNOWN ABOUT THE DISEASE.BRAIN. VOL. 138. ISSUE . P. 2471 -2484 70 80% 8
9 STEVANIN, G , RUBERG, M , BRICE, A , (2008) RECENT ADVANCES IN THE GENETICS OF SPASTIC PARAPLEGIAS.CURRENT NEUROLOGY AND NEUROSCIENCE REPORTS. VOL. 8. ISSUE 3. P. 198 -210 81 80% 31
10 STORTI, E , TESSA, A , PIERELLI, F , MORANI, F , SANTORELLI, FM , DI FABIO, R , (2016) HEREDITARY SPASTIC PARAPLEGIA: PATHOLOGY, GENETICS AND THERAPEUTIC PROSPECTS.EXPERT OPINION ON ORPHAN DRUGS. VOL. 4. ISSUE 4. P. 429 -442 77 75% 0

Classes with closest relation at Level 1



Rank Class id link
1 32627 IGHMBP2//SMARD1//SPINAL MUSCULAR ATROPHY WITH RESPIRATORY DISTRESS
2 22273 ARSACS//AOA2//SENATAXIN
3 20907 OXYSTEROL BINDING PROTEIN//MEMBRANE CONTACT SITES//OSBP
4 2557 SPINOCEREBELLAR ATAXIA//MACHADO JOSEPH DISEASE//SCA2
5 18617 PKAN//NBIA//HALLERVORDEN SPATZ SYNDROME
6 17286 SEIPIN//CONGENITAL GENERALIZED LIPODYSTROPHY//BSCL2
7 5584 ATP DEPENDENT PROTEASE//CLPB//FTSH
8 34724 POLYUNSATURATED FREE FATTY ACID//2 2 DISULFONIC ACID//4 4 DINITROSTILBENE
9 3255 KINESIN//MOLECULAR MOTORS//AXONS AND DENDRITES
10 30096 MARINESCO SJOGREN SYNDROME//SIL1//WARBURG MICRO SYNDROME

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