Class information for:
Level 1: CARNITINE PALMITOYLTRANSFERASE//CARNITINE PALMITOYLTRANSFERASE I//CARNITINE PALMITOYLTRANSFERASE DEFICIENCY

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
8921 1204 33.9 65%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
389 3       PEROXISOME//CARNITINE//JOURNAL OF INHERITED METABOLIC DISEASE 30841
1504 2             CARNITINE//L CARNITINE//TRIMETAZIDINE 7543
8921 1                   CARNITINE PALMITOYLTRANSFERASE//CARNITINE PALMITOYLTRANSFERASE I//CARNITINE PALMITOYLTRANSFERASE DEFICIENCY 1204

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 CARNITINE PALMITOYLTRANSFERASE authKW 901599 7% 44% 80
2 CARNITINE PALMITOYLTRANSFERASE I authKW 312967 3% 34% 36
3 CARNITINE PALMITOYLTRANSFERASE DEFICIENCY authKW 309143 1% 76% 16
4 MALONYL COA authKW 170610 3% 17% 39
5 CARNITINE ACYLTRANSFERASE authKW 158721 1% 48% 13
6 CPT2 authKW 138068 1% 78% 7
7 CARNITINE PALMITYL TRANSFERASE DEFICIENCY authKW 126800 0% 100% 5
8 CARNITINE PALMITOYLTRANSFERASE II authKW 108104 1% 47% 9
9 MITOCHONDRIAL HMG COA SYNTHASE authKW 105665 0% 83% 5
10 MALONYL COA INHIBITION authKW 101440 0% 100% 4

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Biochemistry & Molecular Biology 4939 53% 0% 639
2 Biophysics 1181 12% 0% 147
3 Nutrition & Dietetics 308 5% 0% 58
4 Endocrinology & Metabolism 279 7% 0% 85
5 Medicine, Research & Experimental 216 6% 0% 74
6 Genetics & Heredity 204 7% 0% 82
7 Pediatrics 116 4% 0% 53
8 Clinical Neurology 65 5% 0% 58
9 Cell Biology 59 6% 0% 69
10 Physiology 52 3% 0% 40

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 SW MED SW MED BIOCHEM 50720 0% 100% 2
2 SW MED SW MED GIFFORD S DIABET 50720 0% 100% 2
3 SW MED SW MED INTERNAL MED 50720 0% 100% 2
4 UPR 1524 28916 1% 13% 9
5 ANIM NAT OURCES GROWTH BIOL 25360 0% 100% 1
6 BELLVITGE COLORECTAL CANC STUDY GRP 25360 0% 100% 1
7 BIOCHEM 8701 WATERTOWN PLANK RD 25360 0% 100% 1
8 BRAIN KOREA PROJECT MED SCI 21SEVERANCE MED 25360 0% 100% 1
9 CANADIEN NETWORK EXCELLENCE HUMAN GENET 25360 0% 100% 1
10 CHEM BIOL DATA 25360 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 BIOCHEMICAL JOURNAL 20596 13% 1% 154
2 MOLECULAR GENETICS AND METABOLISM 3551 2% 1% 21
3 BIOCHEMICAL SOCIETY TRANSACTIONS 2561 3% 0% 33
4 BIOLOGY OF THE NEONATE 1903 1% 1% 14
5 JOURNAL OF DEVELOPMENTAL PHYSIOLOGY 1309 0% 1% 6
6 JOURNAL OF BIOLOGICAL CHEMISTRY 1150 7% 0% 87
7 ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS 1126 2% 0% 28
8 JOURNAL OF NUTRITION 1070 2% 0% 24
9 BIOCHIMICA ET BIOPHYSICA ACTA 1029 3% 0% 35
10 BIOCHEMICAL PHARMACOLOGY 957 2% 0% 27

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 CARNITINE PALMITOYLTRANSFERASE 901599 7% 44% 80 Search CARNITINE+PALMITOYLTRANSFERASE Search CARNITINE+PALMITOYLTRANSFERASE
2 CARNITINE PALMITOYLTRANSFERASE I 312967 3% 34% 36 Search CARNITINE+PALMITOYLTRANSFERASE+I Search CARNITINE+PALMITOYLTRANSFERASE+I
3 CARNITINE PALMITOYLTRANSFERASE DEFICIENCY 309143 1% 76% 16 Search CARNITINE+PALMITOYLTRANSFERASE+DEFICIENCY Search CARNITINE+PALMITOYLTRANSFERASE+DEFICIENCY
4 MALONYL COA 170610 3% 17% 39 Search MALONYL+COA Search MALONYL+COA
5 CARNITINE ACYLTRANSFERASE 158721 1% 48% 13 Search CARNITINE+ACYLTRANSFERASE Search CARNITINE+ACYLTRANSFERASE
6 CPT2 138068 1% 78% 7 Search CPT2 Search CPT2
7 CARNITINE PALMITYL TRANSFERASE DEFICIENCY 126800 0% 100% 5 Search CARNITINE+PALMITYL+TRANSFERASE+DEFICIENCY Search CARNITINE+PALMITYL+TRANSFERASE+DEFICIENCY
8 CARNITINE PALMITOYLTRANSFERASE II 108104 1% 47% 9 Search CARNITINE+PALMITOYLTRANSFERASE+II Search CARNITINE+PALMITOYLTRANSFERASE+II
9 MITOCHONDRIAL HMG COA SYNTHASE 105665 0% 83% 5 Search MITOCHONDRIAL+HMG+COA+SYNTHASE Search MITOCHONDRIAL+HMG+COA+SYNTHASE
10 MALONYL COA INHIBITION 101440 0% 100% 4 Search MALONYL+COA+INHIBITION Search MALONYL+COA+INHIBITION

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 BONNEFONT, JP , DEMAUGRE, F , PRIP-BUUS, C , SAUDUBRAY, JM , BRIVET, M , ABADI, N , THUILLIER, L , (1999) CARNITINE PALMITOYLTRANSFERASE DEFICIENCIES.MOLECULAR GENETICS AND METABOLISM. VOL. 68. ISSUE 4. P. 424 -440 96 93% 118
2 MCGARRY, JD , BROWN, NF , (1997) THE MITOCHONDRIAL CARNITINE PALMITOYLTRANSFERASE SYSTEM - FROM CONCEPT TO MOLECULAR ANALYSIS.EUROPEAN JOURNAL OF BIOCHEMISTRY. VOL. 244. ISSUE 1. P. 1 -14 64 70% 932
3 WOLDEGIORGIS, G , DAI, J , ARVIDSON, D , (2005) STRUCTURE-FUNCTION STUDIES WITH THE MITOCHONDRIAL CARNITINE PALMITOYLTRANSFERASES I AND II.MONATSHEFTE FUR CHEMIE. VOL. 136. ISSUE 8. P. 1325-1340 79 90% 5
4 RAMSAY, RR , GANDOUR, RD , VAN DER LEIJ, FR , (2001) MOLECULAR ENZYMOLOGY OF CARNITINE TRANSFER AND TRANSPORT.BIOCHIMICA ET BIOPHYSICA ACTA-PROTEIN STRUCTURE AND MOLECULAR ENZYMOLOGY. VOL. 1546. ISSUE 1. P. 21 -43 101 60% 198
5 SIGAUKE, E , RAKHEJA, D , KITSON, K , BENNETT, MJ , (2003) CARNITINE PALMITOYLTRANSFERASE II DEFICIENCY: A CLINICAL, BIOCHEMICAL, AND MOLECULAR REVIEW.LABORATORY INVESTIGATION. VOL. 83. ISSUE 11. P. 1543-1554 72 77% 34
6 RUFER, AC , THOMA, R , HENNIG, M , (2009) STRUCTURAL INSIGHT INTO FUNCTION AND REGULATION OF CARNITINE PALMITOYLTRANSFERASE.CELLULAR AND MOLECULAR LIFE SCIENCES. VOL. 66. ISSUE 15. P. 2489 -2501 66 69% 14
7 SAGGERSON, D , GHADIMINEJAD, I , AWAN, M , (1992) REGULATION OF MITOCHONDRIAL CARNITINE PALMITOYL TRANSFERASES FROM LIVER AND EXTRAHEPATIC TISSUES.ADVANCES IN ENZYME REGULATION. VOL. 32. ISSUE . P. 285 -306 81 93% 0
8 ZHENG, JL , LUO, Z , ZHU, QL , CHEN, QL , GONG, Y , (2013) MOLECULAR CHARACTERIZATION, TISSUE DISTRIBUTION AND KINETIC ANALYSIS OF CARNITINE,PALMITOYLTRANSFERASE I IN JUVENILE YELLOW CATFISH PELTEOBAGRUS FULVIDRACO.GENOMICS. VOL. 101. ISSUE 3. P. 195-203 39 85% 3
9 FANIN, M , ANICHINI, A , CASSANDRINI, D , FIORILLO, C , SCAPOLAN, S , MINETTI, C , CASSANELLO, M , DONATI, MA , SICILIANO, G , D'AMICO, A , ET AL (2012) ALLELIC AND PHENOTYPIC HETEROGENEITY IN 49 ITALIAN PATIENTS WITH THE MUSCLE FORM OF CPT-II DEFICIENCY.CLINICAL GENETICS. VOL. 82. ISSUE 3. P. 232-239 34 94% 11
10 SAGGERSON, D , (2008) MALONYL-COA, A KEY SIGNALING MOLECULE IN MAMMALIAN CELLS.ANNUAL REVIEW OF NUTRITION. VOL. 28. ISSUE . P. 253-HC3 64 47% 86

Classes with closest relation at Level 1



Rank Class id link
1 37064 MALONIC ACIDURIA//MALONYL COA DECARBOXYLASE DEFICIENCY//MALONYL COA DECARBOXYLASE
2 23687 ACETOACETYL COA SYNTHETASE//ACETOACETYL COA SYNTHETASE AACS//KETONE BODY UTILIZATION
3 973 CARNITINE//L CARNITINE//CARNITINE DEFICIENCY
4 29120 H ATP SYNTHASE//BETA F1 ATPASE MRNA//CSIC BIOL MOLEC BIOL MOLEC
5 2388 NEWBORN SCREENING//MEDIUM CHAIN ACYL COA DEHYDROGENASE DEFICIENCY//UNIT MOL MED
6 17998 ACETYL COA CARBOXYLASE//SORAPHEN A//SORAPHEN
7 29850 MILDRONATE//MET 88//GAMMA BUTYROBETAINE HYDROXYLASE INHIBITOR
8 20822 MCARDLES DISEASE//MYOPHOSPHORYLASE//GLYCOGENOSIS TYPE V
9 24863 PHOSPHATIDATE PHOSPHOHYDROLASE//MED BIOCHEM 328 HERITAGE MED//MED LIPID LIPOPROT GRP
10 14230 BETA KETOTHIOLASE DEFICIENCY//MITOCHONDRIAL ACETOACETYL COA THIOLASE//THIOLASE

Go to start page