Class information for:
Level 2: CONGENITAL ADRENAL HYPERPLASIA//21 HYDROXYLASE DEFICIENCY//ENDOCRINE RESEARCH

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
909 11246 35.6 66%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
284 3       POLYCYSTIC OVARY SYNDROME//ENDOCRINOLOGY & METABOLISM//CORTISOL 42633
909 2             CONGENITAL ADRENAL HYPERPLASIA//21 HYDROXYLASE DEFICIENCY//ENDOCRINE RESEARCH 11246
2552 1                   CONGENITAL ADRENAL HYPERPLASIA//21 HYDROXYLASE DEFICIENCY//CYP21A2 2210
8257 1                   STEROIDOGENIC FACTOR 1//ADRENAL HYPOPLASIA CONGENITA//SF 1 1274
10101 1                   ANTLEY BIXLER SYNDROME//ADRENARCHE//17 ALPHA HYDROXYLASE DEFICIENCY 1092
10728 1                   STEROIDOGENIC ACUTE REGULATORY PROTEIN//STAR//STEROIDOGENIC ACUTE REGULATORY PROTEIN STAR 1040
11446 1                   PNEUMADIN//ADRENAL INNERVATION//LIPID CYTOPLASM RATIO 981
11907 1                   GLOMERULOSA CELLS//ALDOSTERONE SECRETION//ADRENAL GLOMERULOSA 945
14044 1                   19 NORDEOXYCORTICOSTERONE//ALDOSTERONE BIOSYNTHESIS//ALDOSTERONE SYNTHASE DEFICIENCY 796
16517 1                   STUDIES REPROD//MED STUDIES REPROD PHYSIOL//FETAL ZONE 649
16549 1                   ADRENODOXIN//CYTOCHROME P450SCC//ADRENODOXIN REDUCTASE 648
17744 1                   ACTH R//FETAL NEUROENDOCRINOLOGY//MED J HILLIS MILLER HLTH PHYSIOL 584
24408 1                   3 BETA HYDROXYSTEROID DEHYDROGENASE//HSD3B2 GENE//SHORT CHAIN OXIDOREDUCTASE 313
25809 1                   CYP2D16//1 AMINOBENZOTRIAZOLE//2 6 SIALYLATED CELL SURFACE ANTIGEN 271
30277 1                   BRE//BRE GENE//4 AMINOPYRAZOLOPYRIMIDINE 171
31199 1                   HLTH SCI SW MED BIOCHEM//HLTH SCI SW MED OBSTET GYNECOL//20A DIHYDROPROGESTERONE 156
34099 1                   AREA STRUCT FUNCT HUMAN BODY//BIOCHEM BIOCHIM MED//DIET FUNCT FOODS 116

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with term
in class
1 CONGENITAL ADRENAL HYPERPLASIA authKW 1034318 5% 66% 576
2 21 HYDROXYLASE DEFICIENCY authKW 511002 2% 87% 217
3 ENDOCRINE RESEARCH journal 209093 3% 24% 324
4 STEROIDOGENESIS authKW 187242 3% 19% 362
5 ADRENAL CORTEX authKW 182120 2% 30% 222
6 ENDOCRINOLOGY & METABOLISM WoSSC 162480 46% 1% 5194
7 CYP21A2 authKW 136290 1% 80% 63
8 STEROIDOGENIC ACUTE REGULATORY PROTEIN authKW 129390 1% 55% 86
9 ANTLEY BIXLER SYNDROME authKW 124930 0% 87% 53
10 ADRENODOXIN authKW 108908 1% 63% 64

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with term
in class
1 Endocrinology & Metabolism 162480 46% 1% 5194
2 Biochemistry & Molecular Biology 6580 23% 0% 2640
3 Pediatrics 2569 6% 0% 695
4 Cell Biology 2270 9% 0% 1038
5 Reproductive Biology 1639 3% 0% 305
6 Physiology 1503 5% 0% 560
7 Obstetrics & Gynecology 1165 4% 0% 437
8 Anatomy & Morphology 1045 2% 0% 169
9 Biophysics 797 4% 0% 470
10 Genetics & Heredity 516 4% 0% 485

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 PEDIAT ENDOCRINOL 30480 2% 5% 221
2 HLTH SCI SW MED BIOCHEM 25096 0% 49% 19
3 STEROID UNIT 23467 0% 58% 15
4 ADRENAL STEROID DISORDERS PROGRAM 22976 0% 71% 12
5 REPROD ENDOCRINOL SIGNALING GRP 19375 0% 71% 10
6 PEDIAT ENDOCRINOL DIABETOL 18116 0% 17% 39
7 CECIL H IDA GREEN REPROD BIOL SCI 17160 0% 16% 40
8 REPROD DEV SCI CLIN BIOCHEM 15692 0% 64% 9
9 STEROID MASS SPE OMETRY UNIT 13870 0% 32% 16
10 CELL BIOL BIOCHEM 13654 0% 11% 48

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 ENDOCRINE RESEARCH 209093 3% 24% 324
2 JOURNAL OF STEROID BIOCHEMISTRY AND MOLECULAR BIOLOGY 97001 5% 6% 569
3 ENDOCRINOLOGY 58506 7% 3% 735
4 JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM 47114 6% 3% 646
5 MOLECULAR AND CELLULAR ENDOCRINOLOGY 37565 3% 4% 348
6 STEROIDS 18887 2% 4% 175
7 MOLECULAR ENDOCRINOLOGY 17677 2% 3% 193
8 HORMONE RESEARCH 16173 1% 4% 145
9 JOURNAL OF ENDOCRINOLOGY 16051 2% 3% 224
10 JOURNAL OF PEDIATRIC ENDOCRINOLOGY & METABOLISM 12059 1% 4% 127

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 CONGENITAL ADRENAL HYPERPLASIA 1034318 5% 66% 576 Search CONGENITAL+ADRENAL+HYPERPLASIA Search CONGENITAL+ADRENAL+HYPERPLASIA
2 21 HYDROXYLASE DEFICIENCY 511002 2% 87% 217 Search 21+HYDROXYLASE+DEFICIENCY Search 21+HYDROXYLASE+DEFICIENCY
3 STEROIDOGENESIS 187242 3% 19% 362 Search STEROIDOGENESIS Search STEROIDOGENESIS
4 ADRENAL CORTEX 182120 2% 30% 222 Search ADRENAL+CORTEX Search ADRENAL+CORTEX
5 CYP21A2 136290 1% 80% 63 Search CYP21A2 Search CYP21A2
6 STEROIDOGENIC ACUTE REGULATORY PROTEIN 129390 1% 55% 86 Search STEROIDOGENIC+ACUTE+REGULATORY+PROTEIN Search STEROIDOGENIC+ACUTE+REGULATORY+PROTEIN
7 ANTLEY BIXLER SYNDROME 124930 0% 87% 53 Search ANTLEY+BIXLER+SYNDROME Search ANTLEY+BIXLER+SYNDROME
8 ADRENODOXIN 108908 1% 63% 64 Search ADRENODOXIN Search ADRENODOXIN
9 SF 1 101693 1% 51% 74 Search SF+1 Search SF+1
10 DAX 1 98096 0% 80% 45 Search DAX+1 Search DAX+1

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 MILLER, WL , AUCHUS, RJ , (2011) THE MOLECULAR BIOLOGY, BIOCHEMISTRY, AND PHYSIOLOGY OF HUMAN STEROIDOGENESIS AND ITS DISORDERS.ENDOCRINE REVIEWS. VOL. 32. ISSUE 1. P. 81 -151 387 58% 388
2 WHITE, PC , SPEISER, PW , (2000) CONGENITAL ADRENAL HYPERPLASIA DUE TO 21-HYDROXYLASE DEFICIENCY.ENDOCRINE REVIEWS. VOL. 21. ISSUE 3. P. 245 -291 323 68% 607
3 SPEISER, PW , AZZIZ, R , BASKIN, LS , GHIZZONI, L , HENSLE, TW , MERKE, DP , MEYER-BAHLBURG, HFL , MILLER, WL , MONTORI, VM , OBERFIELD, SE , ET AL (2010) CONGENITAL ADRENAL HYPERPLASIA DUE TO STEROID 21-HYDROXYLASE DEFICIENCY: AN ENDOCRINE SOCIETY CLINICAL PRACTICE GUIDELINE.JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM. VOL. 95. ISSUE 9. P. 4133 -4160 168 71% 271
4 MILLER, WL , (2017) DISORDERS IN THE INITIAL STEPS OF STEROID HORMONE SYNTHESIS.JOURNAL OF STEROID BIOCHEMISTRY AND MOLECULAR BIOLOGY. VOL. 165. ISSUE . P. 18 -37 133 55% 2
5 GALLO-PAYET, N , BATTISTA, MC , (2014) STEROIDOGENESIS-ADRENAL CELL SIGNAL TRANSDUCTION.COMPREHENSIVE PHYSIOLOGY. VOL. 4. ISSUE 3. P. 889 -964 310 45% 17
6 FALHAMMAR, H , NORDENSTROM, A , (2015) NONCLASSIC CONGENITAL ADRENAL HYPERPLASIA DUE TO 21-HYDROXYLASE DEFICIENCY: CLINICAL PRESENTATION, DIAGNOSIS, TREATMENT, AND OUTCOME.ENDOCRINE. VOL. 50. ISSUE 1. P. 32 -50 143 82% 2
7 LAVOIE, HA , KING, SR , (2009) TRANSCRIPTIONAL REGULATION OF STEROIDOGENIC GENES: STARD1, CYP11A1 AND HSD3B.EXPERIMENTAL BIOLOGY AND MEDICINE. VOL. 234. ISSUE 8. P. 880 -907 187 54% 104
8 HOIVIK, EA , LEWIS, AE , AUMO, L , BAKKE, M , (2010) MOLECULAR ASPECTS OF STEROIDOGENIC FACTOR 1 (SF-1).MOLECULAR AND CELLULAR ENDOCRINOLOGY. VOL. 315. ISSUE 1-2. P. 27 -39 140 73% 60
9 SCHIMMER, BP , WHITE, PC , (2010) MINIREVIEW: STEROIDOGENIC FACTOR 1: ITS ROLES IN DIFFERENTIATION, DEVELOPMENT, AND DISEASE.MOLECULAR ENDOCRINOLOGY. VOL. 24. ISSUE 7. P. 1322 -1337 123 72% 108
10 STOCCO, DM , (2001) STAR PROTEIN AND THE REGULATION OF STEROID HORMONE BIOSYNTHESIS.ANNUAL REVIEW OF PHYSIOLOGY. VOL. 63. ISSUE . P. 193-213 117 82% 434

Classes with closest relation at Level 2



Rank Class id link
1 3208 DEHYDROEPIANDROSTERONE//DHEA//DEHYDROEPIANDROSTERONE SULFATE
2 1608 POLYCYSTIC OVARY SYNDROME//PCOS//HYPERANDROGENISM
3 2727 11 BETA HYDROXYSTEROID DEHYDROGENASE//11 BETA HYDROXYSTEROID DEHYDROGENASE TYPE 1//11 BETA HSD1
4 760 PHEOCHROMOCYTOMA//PRIMARY ALDOSTERONISM//ADRENOCORTICAL CARCINOMA
5 3042 PERIPHERAL BENZODIAZEPINE RECEPTOR//TSPO//PK11195
6 2373 ADRENAL INSUFFICIENCY//AIRE//APECED
7 772 GRANULOSA CELLS//CORPUS LUTEUM//REPRODUCTIVE BIOLOGY
8 415 CYTOCHROME P450//CYP2D6//PREGNANE X RECEPTOR
9 1407 2 METHOXYESTRADIOL//STEROID SULFATASE//17 BETA HYDROXYSTEROID DEHYDROGENASE
10 1096 SERTOLI CELLS//TESTIS//SPERMATOGONIAL STEM CELLS

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