Class information for:
Level 2: AMYOTROPHIC LATERAL SCLEROSIS//FRONTOTEMPORAL DEMENTIA//ALS

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
699 13006 45.6 82%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
11 4 NEUROSCIENCES//CLINICAL NEUROLOGY//NEUROL 1112395
49 3       ALZHEIMERS DISEASE//AMYOTROPHIC LATERAL SCLEROSIS//DEMENTIA 92146
699 2             AMYOTROPHIC LATERAL SCLEROSIS//FRONTOTEMPORAL DEMENTIA//ALS 13006
402 1                   AMYOTROPHIC LATERAL SCLEROSIS//SOD1//ALS 3530
2623 1                   FRONTOTEMPORAL DEMENTIA//PRIMARY PROGRESSIVE APHASIA//SEMANTIC DEMENTIA 2193
2809 1                   AMYOTROPHIC LATERAL SCLEROSIS//AMYOTROPHIC LATERAL SCLEROSIS AND FRONTOTEMPORAL DEGENERATION//MOTOR NEURON DISEASE 2143
3819 1                   TDP 43//C9ORF72//FUS 1900
7068 1                   AMYOTROPHIC LATERAL SCLEROSIS//PRIMARY LATERAL SCLEROSIS//MOTOR NEURON DISEASE 1409
17353 1                   PROGRANULIN//PGRN//GRANULIN 604
20124 1                   BMAA//BETA N METHYLAMINO L ALANINE//ALS PDC 475
25588 1                   AUDITORY EMOTIONAL STIMULI//AUTOIMMUNE MOTONEURON INJURY//AUTOROSETTE FORMING LYMPHOCYTES 277
26805 1                   WOBBLER MOUSE//T 588//WOBBLER 245
27426 1                   RILUZOLE//PK 26124//1 METHYL 4 PHENYLPYRIDIUM 230

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with term
in class
1 AMYOTROPHIC LATERAL SCLEROSIS authKW 4713394 26% 60% 3370
2 FRONTOTEMPORAL DEMENTIA authKW 1489029 8% 59% 1071
3 ALS authKW 1303369 8% 56% 999
4 MOTOR NEURON DISEASE authKW 1026675 6% 55% 798
5 TDP 43 authKW 962458 4% 81% 504
6 FRONTOTEMPORAL LOBAR DEGENERATION authKW 711204 3% 71% 428
7 PROGRANULIN authKW 617279 2% 92% 287
8 AMYOTROPHIC LATERAL SCLEROSIS AND FRONTOTEMPORAL DEGENERATION journal 531403 2% 79% 286
9 C9ORF72 authKW 473038 2% 92% 220
10 PRIMARY PROGRESSIVE APHASIA authKW 434474 2% 76% 245

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with term
in class
1 Clinical Neurology 159461 48% 1% 6252
2 Neurosciences 69371 43% 1% 5575
3 Geriatrics & Gerontology 8081 4% 1% 584
4 Pathology 6046 7% 0% 874
5 Psychiatry 4495 8% 0% 1005
6 Neuroimaging 1380 1% 0% 185
7 Biochemistry & Molecular Biology 1157 13% 0% 1628
8 Genetics & Heredity 482 4% 0% 525
9 Psychology 444 2% 0% 228
10 Cell Biology 196 4% 0% 550

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with term
in class
1 NEUROL 203898 36% 2% 4663
2 ELEANOR LOU GEHRIG MDA ALS 127273 0% 94% 58
3 MEMORY AGING 123447 1% 28% 186
4 ALS 94863 1% 39% 103
5 SLA 70907 0% 50% 60
6 ALS CLIN 62392 0% 57% 47
7 SHEFFIELD TRANSLAT NEUROSCI SITRAN 56729 0% 55% 44
8 UNIT NEUROL 48364 0% 40% 51
9 NEURODEGENERAT DIS 47992 2% 8% 262
10 FDN SERENA ONLUS 47489 0% 75% 27

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 AMYOTROPHIC LATERAL SCLEROSIS 891238 4% 72% 526
2 AMYOTROPHIC LATERAL SCLEROSIS AND FRONTOTEMPORAL DEGENERATION 531403 2% 79% 286
3 AMYOTROPHIC LATERAL SCLEROSIS AND OTHER MOTOR NEURON DISORDERS 79218 0% 68% 50
4 ACTA NEUROPATHOLOGICA 44777 3% 6% 335
5 JOURNAL OF THE NEUROLOGICAL SCIENCES 42460 3% 4% 430
6 NEUROLOGY 38753 5% 3% 597
7 NEUROBIOLOGY OF AGING 25728 2% 4% 253
8 DEMENTIA AND GERIATRIC COGNITIVE DISORDERS 21601 1% 7% 132
9 JOURNAL OF NEUROLOGY 17864 2% 4% 217
10 JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY 17775 2% 3% 269

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with term
in class
LCSH search Wikipedia search
1 AMYOTROPHIC LATERAL SCLEROSIS 4713394 26% 60% 3370 Search AMYOTROPHIC+LATERAL+SCLEROSIS Search AMYOTROPHIC+LATERAL+SCLEROSIS
2 FRONTOTEMPORAL DEMENTIA 1489029 8% 59% 1071 Search FRONTOTEMPORAL+DEMENTIA Search FRONTOTEMPORAL+DEMENTIA
3 ALS 1303369 8% 56% 999 Search ALS Search ALS
4 MOTOR NEURON DISEASE 1026675 6% 55% 798 Search MOTOR+NEURON+DISEASE Search MOTOR+NEURON+DISEASE
5 TDP 43 962458 4% 81% 504 Search TDP+43 Search TDP+43
6 FRONTOTEMPORAL LOBAR DEGENERATION 711204 3% 71% 428 Search FRONTOTEMPORAL+LOBAR+DEGENERATION Search FRONTOTEMPORAL+LOBAR+DEGENERATION
7 PROGRANULIN 617279 2% 92% 287 Search PROGRANULIN Search PROGRANULIN
8 C9ORF72 473038 2% 92% 220 Search C9ORF72 Search C9ORF72
9 PRIMARY PROGRESSIVE APHASIA 434474 2% 76% 245 Search PRIMARY+PROGRESSIVE+APHASIA Search PRIMARY+PROGRESSIVE+APHASIA
10 SOD1 420685 2% 58% 311 Search SOD1 Search SOD1

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 COZZOLINO, M , PESARESI, MG , GERBINO, V , GROSSKREUTZ, J , CARRI, MT , (2012) AMYOTROPHIC LATERAL SCLEROSIS: NEW INSIGHTS INTO UNDERLYING MOLECULAR MECHANISMS AND OPPORTUNITIES FOR THERAPEUTIC INTERVENTION.ANTIOXIDANTS & REDOX SIGNALING. VOL. 17. ISSUE 9. P. 1277 -1330 402 70% 18
2 LING, SC , POLYMENIDOU, M , CLEVELAND, DW , (2013) CONVERGING MECHANISMS IN ALS AND FTD: DISRUPTED RNA AND PROTEIN HOMEOSTASIS.NEURON. VOL. 79. ISSUE 3. P. 416-438 177 73% 265
3 TURNER, BJ , TALBOT, K , (2008) TRANSGENICS, TOXICITY AND THERAPEUTICS IN RODENT MODELS OF MUTANT SOD1-MEDIATED FAMILIAL ALS.PROGRESS IN NEUROBIOLOGY. VOL. 85. ISSUE 1. P. 94 -134 283 71% 255
4 MACKENZIE, IRA , RADEMAKERS, R , NEUMANN, M , (2010) TDP-43 AND FUS IN AMYOTROPHIC LATERAL SCLEROSIS AND FRONTOTEMPORAL DEMENTIA.LANCET NEUROLOGY. VOL. 9. ISSUE 10. P. 995-1007 174 91% 304
5 RASCOVSKY, K , HODGES, JR , KNOPMAN, D , MENDEZ, MF , KRAMER, JH , NEUHAUS, J , VAN SWIETEN, JC , SEELAAR, H , DOPPER, EGP , ONYIKE, CU , ET AL (2011) SENSITIVITY OF REVISED DIAGNOSTIC CRITERIA FOR THE BEHAVIOURAL VARIANT OF FRONTOTEMPORAL DEMENTIA.BRAIN. VOL. 134. ISSUE . P. 2456 -2477 135 87% 529
6 LAGIER-TOURENNE, C , POLYMENIDOU, M , CLEVELAND, DW , (2010) TDP-43 AND FUS/TLS: EMERGING ROLES IN RNA PROCESSING AND NEURODEGENERATION.HUMAN MOLECULAR GENETICS. VOL. 19. ISSUE . P. R46-R64 192 76% 334
7 WIJESEKERA, LC , LEIGH, PN , (2009) AMYOTROPHIC LATERAL SCLEROSIS.ORPHANET JOURNAL OF RARE DISEASES. VOL. 4. ISSUE . P. - 196 82% 299
8 SEELAAR, H , ROHRER, JD , PIJNENBURG, YAL , FOX, NC , VAN SWIETEN, JC , (2011) CLINICAL, GENETIC AND PATHOLOGICAL HETEROGENEITY OF FRONTOTEMPORAL DEMENTIA: A REVIEW.JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY. VOL. 82. ISSUE 5. P. 476 -486 179 90% 163
9 REDLER, RL , DOKHOLYAN, NV , (2012) THE COMPLEX MOLECULAR BIOLOGY OF AMYOTROPHIC LATERAL SCLEROSIS (ALS).MOLECULAR BIOLOGY OF NEURODEGENERATIVE DISEASES. VOL. 107. ISSUE . P. 215 -262 263 75% 44
10 ROBBERECHT, W , PHILIPS, T , (2013) THE CHANGING SCENE OF AMYOTROPHIC LATERAL SCLEROSIS.NATURE REVIEWS NEUROSCIENCE. VOL. 14. ISSUE 4. P. 248 -264 156 68% 274

Classes with closest relation at Level 2



Rank Class id link
1 1735 SPINAL MUSCULAR ATROPHY//CHARCOT MARIE TOOTH DISEASE//NEUROFILAMENT
2 823 DIFFUSION TENSOR IMAGING//TRACTOGRAPHY//ALZHEIMERS DISEASE
3 3249 HIRAYAMA DISEASE//POSTPOLIOMYELITIS SYNDROME//POST POLIO SYNDROME
4 2650 EXTRACELLULAR SUPEROXIDE DISMUTASE//SUPEROXIDE DISMUTASE//SOD MIMIC
5 166 PARKINSONS DISEASE//MOVEMENT DISORDERS//MULTIPLE SYSTEM ATROPHY
6 1645 HUNTINGTONS DISEASE//HUNTINGTIN//POLYGLUTAMINE
7 35 ALZHEIMERS DISEASE//AMYLOID PRECURSOR PROTEIN//TAU
8 1711 SPINOCEREBELLAR ATAXIA//HEREDITARY SPASTIC PARAPLEGIA//FRIEDREICHS ATAXIA
9 3956 RKIP//RAF KINASE INHIBITOR PROTEIN//HIPPOCAMPAL CHOLINERGIC NEUROSTIMULATING PEPTIDE
10 838 DEMENTIA//GERONTOLOGY//APATHY

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